Hereditary transthyretin(hATTR)amyloidosisis a rare progressive disease that is passed from parent to child.
Normal TTR bringsthyroid hormoneandvitamin Ato body tissues.
The damaged form is more likely to have an odd structure and misfold.
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When TTR misfolds, it collects in clusters called amyloid deposits.
These clumps can prevent normal function of your heart, nerves, and other body tissue.
For some people, newtreatmentscan impact the effect of the disease and help improve outcomes.
This article describes hATTR and how it affects your life expectancy.
It also describes factors that impact your lifespan and ways to cope with this severe condition.
However, its important to consider that hATTR amyloidosis is a highly heterogeneous disease.
With a wide range of mutations, this disease can affect everyone differently.
Life expectancy is affected by the organs damaged at baseline and through disease progression in hATTR amyloidosis.
Survival Rate
A disease prognosis can involve several types of projections regarding likely outcomes.
Two common measurements of disease outcomes are life expectancy andsurvival rates.
Survival rates are not related to a cure or treatment.
Factors Influencing hATTR Amyloidosis Life Expectancy
The condition hATTR amyloidosis affects everyone uniquely.
Many factors can impact how hATTR amyloidosis affects your life expectancy.
Below are details on factors that may influence your life expectancy.
When amyloid deposits form in your heart, they can make the walls thick and stiff.
The result can lead toheart failure.
This is a condition in which your heart is unable to pump blood through your body effectively.
For some people, symptoms may never occur.
Research indicates that having early-onset hATTR amyloidosis may predispose you to less-severe symptoms.
Treatments Used
Treatment pop in may impact life expectancy.
Research indicates these novel therapies can improve quality of life and sometimes increase survival rates.
Manage stress: Dealing with a chronic conditions physical and emotional toll can increase stress.
While an early diagnosis and treatment can help improve your outcomes, the details can be complex.
Factors such as your exact gene variant and the age of disease onset can impact your outcomes.
The wide range of variants means no one common outcome for this disease exists.
Given all these factors, discussing concerns about your mortality with your healthcare provider before making assumptions is key.
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